全部文献期刊学位论文会议报纸专利标准年鉴图书|学者科研项目
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作者:C. Wary , N. Azzabou ...
来源:[J].Neuromuscular Disorders(IF 3.464), 2014, Vol.24 (9-10), pp.853-853Elsevier
摘要:The evolution of quantitative NMR imaging (NMRI) and spectroscopy (NMRS) indices over one year is reported in forearms of 21 Duchenne Muscular Dystrophy (DMD) patients amenable to exon 53 skipping therapy. Patients aged 6 to 18 yrs, 12 non-ambulant at inclusion, were followe...
作者:C. Wary , B. Matot ...
来源:[J].Neuromuscular Disorders(IF 3.464), 2014, Vol.24 (9-10), pp.822-822Elsevier
摘要:We have previously demonstrated that a recombinant adeno-associated virus vector, serotype 8 (rAAV8) carrying a modified U7snRNA sequence promoting exon skipping injected in GRMD by locoregional transvenous perfusion of the forelimb, restores up to 80% dystrophin expression ...
作者:C. Wary , N. Azzabou ...
来源:[J].Neuromuscular Disorders(IF 3.464), 2013, Vol.23 (9-10), pp.810-810Elsevier
摘要:Non-invasive measurements and quantitative evaluation of the natural course of disease need to be established in anticipation of replacement therapy in Duchenne muscular dystrophy (DMD). A cohort of 23 DMD boys (6–18 years, 14 non-ambulant), were enrolled specifically to cha...
作者:... A.B. Martins-Bach , C. Wary , P.G. Carlier
来源:[J].Neuromuscular Disorders(IF 3.464), 2012, Vol.22 (9-10), pp.822-823Elsevier
摘要:Abstract(#br)The mdx mouse remains a popular model of the Duchenne muscular dystrophy. While criticized for the mild impairment of muscle function and structure, the mdx remains highly relevant in terms of energy and microvascular control disturbances associated to muscle dy...
作者:C. Wary , D. Orlikowski
来源:[J].Neuromuscular Disorders(IF 3.464), 2013, Vol.23 (9-10), pp.828-828Elsevier
摘要:Skeletal muscle NMR imaging has two distinct roles: 1/ to diagnose disorders and 2/ to monitor disease progression. Both have been played to the benefit of type II glycogenosis patients (GSDII). In this study, we quantified muscle water T2, a marker of disease activity, in thigh ...
作者:C. Wary , S. Moullec ...
来源:[J].Neuromuscular Disorders(IF 3.464), 2012, Vol.22 (9-10), pp.859-859Elsevier
摘要:Abstract(#br)Replacement therapy of dystrophinopathies has begun with promising results both in animals and in patients. Non-invasive quantitative tools are needed to evaluate its potential benefits or side effects but also to determine the optimal protocol. Fifteen GRMD dogs wer...
作者:C. Wary , J. Pariès ...
来源:[J].Diabetes and Metabolism(IF 2.388), 2012, Vol.38, pp.A11-A11Elsevier
摘要:Introduction(#br)Nous avons précédemment montré que les diabétiques de type 2 (DT2) présentaient une capacité oxydative mitochondriale altérée qui semblait associée essentiellement au déséquilibre glycémique. L’objectif était ici d’examiner les liens entre per...

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